Title : Extradural myxopapillary ependymoma - A case report
Abstract:
Introduction:
Myxopapillary ependymoma is a specific type of ependymoma that in very rare cases can occur in the extraspinal soft tissues. Categorized as Grade I lesions myxopapillary ependymomas are considered benign but are capable of local recurrence, dissemination and a more aggressive disease course.
Case:
The patient is a six year old boy with a formation in the sacral area with approximate dimensions 5x5cm. Primary suspicion was hematoma because of history of repeated trauma to the buttocks. Ultrasonographic and Computed Tomography scans revealed the precise location, size and blood supply of the tumor. Gross- total resection was attempted.
Results:
The sacrum and coccygeal bone were found to be intact and en-bloc resection was feasible. Histopathological result indicated extramedullary myxopapillary ependymoma. Postoperative period was uneventful. Follow-up Magnetic Resonance scan revealed normal postoperative finds and no signs of residual formation and/or recurrence.
Conclusions:
Even though a very rare tumor, ME should be considered a possibility for sacral region tumors. Keeping in mind the potential of the tumor for local recurrence and metastases, it is advised that extradural subcutaneous ME be considered a low-grade malignant tumor and gross-total excision should be performed in all cases. Periodical postoperative examination is warranted for long term tumor control.
Audience Takeaway Notes:
- We hope to draw their attention to a rare tumor with more malignant potential than the usual benign tumor.
- And by raising awareness we hope for better outcome
